Hemophagocytic lymphohistiocytosis associated with Behçet"(TM)s syndrome in a female patient with a history of rheumatoid arthritis

  • Juan Carlos Soto Universidad Libre, Barranquilla, Colombia
  • Andrés Mier Universidad Libre, Barranquilla, Colombia
  • Rawdy Reales Universidad Libre, Barranquilla, Colombia
  • Karen Vibanco Universidad Libre, Barranquilla, Colombia
  • Carlos Barrera Universidad Libre, Barranquilla, Colombia
  • Felipe González Organización Clínica General del Norte, Barranquilla, Colombia

Abstract

Hemophagocytic lymphohistiocytosis can appear as a complication due to immune hyperreactivity in the context of loss of tolerance to own structures as in collagen diseases. The case of a 62-year-old woman with a history of rheumatoid arthritis who meets diagnostic criteria for Behçet"(TM)s disease is presented. After haematological complications and complementary studies, phagocytes with medullary hyperreactivity are documented as a cause of cytopenias, generating the diagnosis of hemophagocytic lymphohistiocytosis. With the present case, it is intended to emphasize the association of hematological and inflammatory alterations in patients with autoimmune disease

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Author Biographies

Juan Carlos Soto, Universidad Libre, Barranquilla, Colombia
Residente Medicina Interna
Carlos Barrera, Universidad Libre, Barranquilla, Colombia
Coordinador programa de medicina interna.
Felipe González, Organización Clínica General del Norte, Barranquilla, Colombia
Jefe de medicina interna
Published
2019-05-20
How to Cite
Soto, J. C., Mier, A., Reales, R., Vibanco, K., Barrera, C., & González, F. (2019). Hemophagocytic lymphohistiocytosis associated with Behçet"(TM)s syndrome in a female patient with a history of rheumatoid arthritis. Acta Médica Colombiana, 43(1S), 42-45. https://doi.org/10.36104/amc.2018.1361